[sci.med] Red Blood Cell Destruction

bs@linus.UUCP (Robert D. Silverman) (11/10/86)

A friend of mine has just been diagnosed as having a VERY rare blood
disorder known as nocturnal hemoglobin urea. I heard a lecture on
the genetics of this disorder by Prof. Paul Levine back when I was
studying biochemistry. I only remember his comments vaguely but it
seems that the disorder has a purely genetic cause. The order with
which the lipo-proteins (particularly spectrin) are inserted into
the cell walls (red blood corpuscles) when they are manufactured is
somehow 'mixed up'. This in turn somehow weakens the cell walls in a
way that wasn't understood then.
The disorder results from certain chemicals released during sleep.
They somehow interact with the weakened red blood cell walls and cause
them to lyse during sleep.

Note: I'm not sure I have all the details correct.

Query: Is anything else known about this disorder? What is known
about treatment, prognosis, etc.

Bob Silverman

bs@linus.UUCP (11/22/86)

Isn't anyone going to respond to my query about Nocturnal Hemoglobin urea?

Bob Silverman